About Thalassaemia (Sinhala)

Page 1








mgqk mßÉfþoh

01' jk mßÉfþoh reêrh wfma Ôjkd,shhs' reêrfha ld¾hNdrh' reêrfha ixhq;sh' reêrh ^iïmq¾K&' reêr j¾.h $ >Kh' reêrh iïnkaê; frda.' uyd ;e,isñhdj'

msgq wxl

^01-08&

2' jk mrssÑfþoh ^09-22& cdK úoHdj yd ;e,iSñhdj' cdk' uyd ;e,isñhdj iE§ug fya;=jk r;= reêrdkqfõ úlD;sh' ysfuda.af,dìka yd hlv' ;e,iSñhdfõ pathophysiology-ìgd oï je,a ke;slu yd we,a*d oïje,a jeä ùu' ;e,iSñhdj frda. ^úksYaph yÿkd .eksu& uyd ;e,iSñhdj frda. úksYaph ioyd ks;r Ndú;d lrk reêr mßËK' uyd îgd ;e,iSñhdj ioyd m%;sldr' 3' jk mrssÑfþoh ^23-39& reêr mdrú,hk m%;sldrh' reêr mdrú,hkh mgka .; hq;af;a l=uk wjia:dfõ§o? wdrlaId iys; reêr mdrú,hkhla ia:dms; lsÍu' reêr .Kh iïnkaO cdk úoHdj' mdrú,hkh l, hq;af;a fudkjdo? reêr mdrú,hk l%ufõo ilia lsßu' reêr mdrú,hkh id¾:l;ajh we.hSu' reêr mdrú,hk m%;sls%hd j,g m%;sldr lsßu'


4' jk mßÉfþoh ^40-71& hlv w;sßla;hka tl;=ùu yd hlv Yßrfhka bj;a lsßu' ksfrda.S mqoa.,hl=f.a YÍrfha we;s hlv' ;e,iSñhd frda.shl=f.a Yßrfha hlv' jeämqr tl;=jk hlv Yßrhg ydks lrk whqre' fviaf*rsTlaióka ^bxfclaIka& DFO' hlv bj;alsßfï m%;sldr mgka .kafka fldhs ld,fhao? fviaf*rsTlaióka §fï ;j;a l%u' fviaf*rsTlaióka m%;sldrfha id¾:l;ajh we.hSu' fviaf*rsTlaieóka ud;%dj fjkialsßug reêrfha f*ßàka uÜgu Ndú;d lsßu' uQ;%d j, we;s hlv uÜgu' fviaf*rsTlaieóka j, we;s ixl=,;d yd tajd n,d.kakd l%u$.eì .ekSsu' fviaf*rsTlaieóka m%;sldrhg wkql+,;djh' hlv bj;a lsÍug we;s wfkl=;a T!IO' fvf*ßfm%dkaj, ^fm;s& L1 j, l%shdldÍ;ajh' fvf*ßfm%dkaj, ^fm;s& j, w;=re m%ÓM,' fvf*ßfm%dkaj, ld¾HlaIu;djh' hlv bj;a lsÍug we;s w¿;a T!IO' 5' jk mßÉfþoh ^72-88& ;e,iSñhd frda.h iïnkaO ffjoHuh' .eg¿ yd tajdg m%;sldr' ma,Sydfõ wêl%shdldÍ;ajh' ma,Sydj bj;a lsÍu yd wdidok' yDoh jia;=j yd wka;rdi¾. .%kaÝj, ixl=,;d' yDoh jia;=fõ ixl=,;d' wka;rdi¾. .%kaÝkaays ixl=,;d' 6' jk mßÉfþoh ^89-103& ;e,iSñhd frda.SkAf.a wdidok' reêr mdrú,hkh iïnkaO wdidok' fymghsáia î wdidokh' wfkl=;a jhsrihka' w`t;a frda. ldrlhka mrk frda. ldrl ms<sno w`t;a lkiai,a,' reêrfha wdrlaIdldß nj' wdrlaIdldß nj yd reêr m%udkd;aul nj' m%;sldr fkdl, ;e,isñhd frda.sfhl=g isÿjk foa ms,sno idrxYhla'


7' jk mßÉfþoh ^104-109& uOHu ;e,iSñhdj yd wfkl=;a ;e,iSñhd frda.' frda. úksYaph' uOHu ;e,isñhdjg m%;sldr lsßu' hlv bj;a lsßfï m%;sldr' uOHu ;e,iSñhdfõ ffjoHuh .eg`t' widudkH ysfuda.af,daîka fyda jHqyd;aul fjkila we;s ysfuda.af,dìka ksid we;sjk ;e,isñhdj' îgd ;e,iSñhdj yd widudkH ysfud.af,dìka ixhqla; úu' we,a*d ;e,isñhdj' 8' jk mßÉfþoh ^110-116& ia:dms; yd wkd.;fha n,dfmdfrd;a;= ;eìh yels m%;sldr l%u' 9' jk mßÉfþoh fjk;a m%;sldr l%u'

^117-1168&

10' jk mßÉfþoh udkisl yd iudÔh .eg`M'

^119-124&

11' jk mßÉfþoh w;sf¾l f;dr;=re'

^125-129&

12' jk mßÉfþoh ;e,isñhd frda. jHdma;sh yd th je,elaùu'

^130-146&

13' jk mßÉfþoh wdydr yd ;e,isñhdj' 14' jk mßÉfþoh MRT T2* u.ska yDofha we;s hlv uekSu'

^147-152& ^153-154&

15' jk mßÉfþoh ^155-161& hlv wêNdrh yd thg m%;sldr ms<sno idrdxYh' uyd ;e,isñhd frd.skag m%;sldr lsßu ms<snoj .e,Sï igyk' fviaf*ßTlaióka' fv*ßfm%dka' fv*ßisfrdlaia'


16' jk mßÉfþoh fma%fya,sldj'

^162-164&

17' jk mßÉfþoh jeo.;a fjí msgq yd ,smskhka'

^165-166&

18' jk mßÉfþoh Useful Correspondence and Information

^167-171&







1a

1b

1


1c

1d

1e

2


1g

1f

3


1h

1f

4


1i

1j

1k

1l

5


1m

6


1w

7


8


2a

9


2b

2c

10


2d

11


2e 12


2f

13



15





jhi

uyd ;e,iSñhdj

uOHu ;e,iSñhdj

wjqreoaog wvq

62-75%

4-11%

wjqreÿ 1 - 2 w;r

29-35%

11-30%

wjqreÿ 2 g jeä

9-11%

22-59%


uOHia: w.h

mrdih

ysfud.af,daîka (Hb) .%Eï /ñ',s 100 g

6.8

3.9 - 9.3

tï iS tÉ msfld.%Eï

20.9

15 - 26

tï iS ù *e,eïfgd ,Sg¾

65.8

57 - 75

tï iS tÉ iS .%Eï /ñ',S 100 g

30.9

26 - 34

20



22


23


24


25


26


27


28


29


30


odhl reêrfha ysufgdls%Ü yd ,nd Èh hq;= mßudj ls'.%E'$ó',S'j,ska'

80% 2.6 5.2 7.8 10.4


32







38


39



41



2

3+

2

2+ 2 2

2+

" -

"

-

3+



45


46


47


48


49


50


51



53



55


56


4g

57


58


59


60


4h

61


62


63.


4j

64


65


66


67


4k

68


69


70


71


72


5b

73


74


75


1'yDowlrksh ^oaúfldaIsl&

yDo jia;=j


5c

77


78


79


80


j¾Okh yd mßjD;a;sh ls%hdj, fõ.h md,kh f,a j, le,aishï m%udkh md,kh

f,a j, fidaähï yd laf,drhsâ md,kh YÍrh wd;;sl wjia;d i`oyd iqodkï lrhs msßñkaf.a oaú;shsl ,sx.sl ,CIK we;s lrhs .eyekq whf.a oaú;shsl ,sx.sl ,CIK we;s lrhs l,,h ;ekam;a úug .¾NdYh iqodkï lrhs wfkl=;a wka;rdi¾. .%kaÓ md,kh lrhs


82


83


84


85


5e

5f

86


87


88


89


90


91


92


6a

93


6b

94


6c

6d

95


6e

6f 96


97


6g

98


99


100


101


102


;e,isóhd frda.Skag m%;sldr fkdlsßfuka we;sjk ixl=,;d ms<sno idrdxYh

msáhqgß .%kaÓh ^j¾Okh" ,sx.sl wjhj weâä%k,a .%ksÓh yd ;hsfrdhsvhg n,mEu&

uqyqfka úlD;s ùu ^Wvq ykqj uy;afõ&

;hsfrdahsâ .%kaÓh ^l,d;=rlska muks& merd ;hsfrdahsâ .%kaÓ ^l,d;=rlska muk& yDoh ^yDo wlrKsh" jeo.;au ixl=,;djh & wlaudj ^uy;aùu&

ma,sydj ^mÜáld wvq fõ&

w.akHdih ^Èhjeähdj& reêrh ^rla;ysk;djh& yu ^ÿ¾j¾K ùu& ,sx.sl wjhj ^j¾Okh"ls%hdldß;ajh wvd, fõ& wiaÓ ^fõokdj yd TiaáfhdafmdfrdaiSia &

wiaÓ N.akh fõ j¾Ol w.% ^l,ska jeisu&

103


104


105



107


108


109


8a

8b

110


111


8c 112


fmidfrdaf.a w;aoelï jhi 16g wvq ,uqka

ixLHdj

Ôj;ajk m%;sY;h 95]

ixl=,;d rys; m%;sY;h

Ldkavh 1 Ldkavh 2 Ldkavh 3

121 272 125

85] 78]

90] 81] 59]

jhi 16g jeä

70

70]

66]

113


114


115


116


117


118


119


120


121


122


123


124


125




128


129


12a

12b

130


12c

131



133


134


135


136


137


138


139



12e

12f

141


142


143


144


145


146


147


148


149


150


151


152


153


154



156





160


161



163












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